Vol. 20 No. 2 (2021)
Clinical Cases

Canvas: A case report

Published 2022-01-04

Keywords

  • CANVAS,
  • Vestibular areflexia,
  • Vídeo head impulse test,
  • Vestibulo-ocular reflex,
  • Dizziness,
  • Vestibulo hypofunction
  • ...More
    Less

How to Cite

1.
A. L. T. Silva L, M. Lapenta M, C. Martins AC, D. Rocha G, Kaefer C, da Silveira LC, P. Barbosa MN. Canvas: A case report. BJHBS [Internet]. 2022 Jan. 4 [cited 2024 Oct. 11];20(2):167-71. Available from: https://bjhbs.hupe.uerj.br/bjhbs/article/view/40

Abstract

CANVAS is an acronym for cerebellar ataxia, neuropathy and vestibular areflexia syndrome that was recently described in 2011. This paper reports a case of a 69 years old female that presented a history of dizziness for 9 years, associated with altered vestibulo-ocular reflex (VVOR) and bilateral hypo-functiom at video head impulse test (vHIT), wicth confirmed CANVA syndrome. Imbalance is a consistent symptom of CANVAS and, in most cases, it is the first to manifest. Its presentation demonstrates the importance of the specialist’s need for knowledge of this clinical condition to enable an assertive diagnosis.

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References

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